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ALS-causing mutations differentially affect PGC-1 alpha expression and function in the brain vs. peripheral tissues

Erstveröffentlichung
2017
Authors
Bayer, Hanna
Lang, Kerstin
Buck, Eva
Higelin, Julia
Barteczko, Lara
et al.
Wissenschaftlicher Artikel


Published in
Neurobiology of Disease ; 97 (2017), A. - S. 36-45. - ISSN 0969-9961. - eISSN 1095-953X
Link to publication
https://dx.doi.org/10.1016/j.nbd.2016.11.001
Faculties
Medizinische Fakultät
Institutions
UKU. Klinik für Neurologie
Institut für Anatomie und Zellbiologie
UKU. Abteilung für Gentherapie
Core Facility Genomics
DFG Project THU
GRK 1789 / CEMMA / Zelluläre und molekulare Mechanismen der Alterung / DFG / 194266605
Subject headings
[Free subject headings]: Amyotrophic lateral sclerosis | Lou Gehrig disease | PGC-1 alpha | Lactate | FUS | SOD1 | amyotrophic-lateral-sclerosis | mitochondrial biogenesis | mouse model | superoxide-dismutase | huntingtons-disease | energy-metabolism | coactivator pgc-1 | gene-expression | l-lactate | muscle
[DDC subject group]: DDC 610 / Medicine & health

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